Name : Morteza
Family : Sanei Taheri
Affiliation :Radiology Department,Shohada Tajrish Hospital,SBMU
Academic Degree : Associate Professor of Radiology
Resident : abed mehrvar
Head & Neck Imaging
Gender : Male
Age : 21
21 y/o man with history of Ewing’s sarcoma present headache, Right sided ptosis and mydriasis and oropharyngeal dysphagia.
CT scan demonstrate soft tissue masss in Rt nasopharynx with bone destruction in clivus and petrous and encasement of C2 part of ICA and extention to jugular foramen MRI and MRV: partial visualization of right sigmoid sinus with non visualized Rt jugular vein due to tumor invasion and thrombosis
Metastatic Ewing sarcoma & Sinus thrombosis
Discussion (Related Text)
Ewing sarcoma is the second most common highly malignant primary bone tumour of childhood after osteosarcoma, typically arising from medullary cavity with invasion of Haversian system. They usually present as moth-eaten destructive permeative lucent lesions in the shaft of long bones with large soft tissue component without osteoid matrix, and typical onion skin periostitis Prognosis is significantly impacted by the presence of distant metastases at the time of diagnosis, which are far more common for the pelvis (25-30%) compared to extremities (<10%) 5. metastases most frequently go to bone or lungs. the skull base and nasopharyngeal metastasis is rare.
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